Acessibilidade / Reportar erro
Continuing Medical Education • An. bras. dermatol. 88 (2) • Apr 2013 • https://doi.org/10.1590/S0365-05962013000200001   copy

Inherited epidermolysis bullosa: clinical and therapeutic aspects* * Work conducted at the Service of Dermatology, Complexo Hospitalar Universitário Prof. Edgard Santos, Federal University of Bahia (C-HUPES-UFBA) - Salvador (BA), Brazil.

Epidermólise bolhosa hereditária: aspectos clínicos e terapêuticos

Authorship SCIMAGO INSTITUTIONS RANKINGS

Inherited epidermolysis bullosa (EB) is a heterogeneous group of genetic disorders that present with skin and, in some cases, mucosal fragility, predisposing patients to the development of blisters and/or erosions after minimal trauma or friction. Children with a recurrent history of these kinds of lesions or neonates that present them in the absence of another reasonable explanation should be investigated. Diagnosis must be based on clinical and histopathological findings. To date, management of inherited EB basically consists in avoiding traumas that trigger lesions, as well as preventing infection and facilitating healing of the wounds with the systematic use of bandages.

Epidermolysis bullosa; Epidermolysis bullosa dystrophica; Epidermolysis bullosa, junctional; Epidermolysis bullosa simplex

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