Type 1 diabetes mellitus (DM1) is one of the most important pediatric endocrinology diseases. It has different kinds of manifestation, such as systemic disturbances caused by poor glycemic control, like hepatomegaly and dwarfism. The outcome of 8 years of poor glycemic control with clinical and laboratory signs suggesting Mauriac's syndrome is presented. This is an uncommon form of DM1. The aim of this study is to update, guide and answer some doubts of professionals with regard to diagnosis and treatment of cases of Mauriac's syndrome.
Diabetes mellitus type 1; Diabetic glucogenosis; Hepatomegaly; Mauriac's syndrome
