Resumos
São relatados 4 casos de miopatia ocular descendente (MOD) com história familial levantada em três gerações. Biópsia musculares e eletromiografia em um caso confirmaram o caráter miogênico da doença. A MOD nada mais seria do que uma forma clínica especial de distrofia muscular, de início tardio.
Four cases of the so-called descending ocular myopathy with a family history in three generations are reported. In the first case muscular biopsy and electromyographic studies proved the myogenic nature of the process. Descending ocular myopathy seems to be just a clinical form of muscular distrophy of late onset.
Miopatia ocular descendente
Descending ocular myopathy
Nunjo FinkelI; Antonio R. Vaz RibeiroII; Maria C. Rodrigues SampaioII
IClínica Neurológica do Hospital dos Servidores do Estado (Rio de Janeiro, GB)
IIClínica Neurológica do Hospital dos Servidores do Estado (Rio de Janeiro, GB); Médicos residentes
RESUMO
São relatados 4 casos de miopatia ocular descendente (MOD) com história familial levantada em três gerações. Biópsia musculares e eletromiografia em um caso confirmaram o caráter miogênico da doença. A MOD nada mais seria do que uma forma clínica especial de distrofia muscular, de início tardio.
SUMMARY
Four cases of the so-called descending ocular myopathy with a family history in three generations are reported. In the first case muscular biopsy and electromyographic studies proved the myogenic nature of the process. Descending ocular myopathy seems to be just a clinical form of muscular distrophy of late onset.
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Clínica Neurológica Hospital dos Servidores do Estado 20000 Rio de Janeiro, GB Brasil.
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Datas de Publicação
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Publicação nesta coleção
17 Abr 2013 -
Data do Fascículo
Jun 1972