Resumo
A case of primary extragonadal yolk sac tumor in the retroperitoneum of a young adult male is reported. The symptoms were melena and weakness for two months. Radiologic studies suggested a retroperitoneal tumor infiltrating the duodenum, artery aorta and vein cava, was found. Partial resection was performed, remaining tumor around the vessels. Microscopic examination disclosed a yolk sac tumor infiltrating the duodenum. The patient was managed unsuccessfully with radiotherapy, but good results were actived with chemotherapy. Few cases like that were reported in the literature.
Endotermal sinus tumor; Yolk sac tumor; Retroperitoneal neoplasms
Endotermal sinus tumor; Yolk sac tumor; Retroperitoneal neoplasms
RELATOS DE CASOS
Tumor do saco vitelino primário em retroperitônio
Primary retroperitoneal yolk sac tumor
Ascêncio Garcia Lopes JuniorI; José Pontes JúniorII; Fernanda CavalcantiIII; Paulo David Branco, ECBC-SPIV; Aldo Junqueira Rodrigues Júnior, TCBC-SPV; Dario Birolini, TCBC-SPVI
IPreceptor de Cirurgia Geral do Departamento de Cirurgia da FMUSP
IIResidente de Cirurgia Geral do Departamento de Cirurgia da FMUSP
IIIMédica do Serviço de Anatomia Patológica do Hospital das Clínicas da FMUSP
IVProfessor Associado da Disciplina de Cirurgia Geral do Departamento de Cirurgia da FMUSP
VProfessor Titular da FMUSP e Chefe do Departamento de Cirurgia
VIProfessor Titular da Disciplina de Cirurgia Geral e do Trauma do Departamento de Cirurgia da FMUSP
Endereço para correspondência Endereço para correspondência: Dr. Ascêncio G. Lopes Júnior Rua Adhemar P. Barros, 387 86050-160 - Londrina - PR
ABSTRACT
A case of primary extragonadal yolk sac tumor in the retroperitoneum of a young adult male is reported. The symptoms were melena and weakness for two months. Radiologic studies suggested a retroperitoneal tumor infiltrating the duodenum, artery aorta and vein cava, was found. Partial resection was performed, remaining tumor around the vessels. Microscopic examination disclosed a yolk sac tumor infiltrating the duodenum. The patient was managed unsuccessfully with radiotherapy, but good results were actived with chemotherapy. Few cases like that were reported in the literature.
Key words: Endotermal sinus tumor; Yolk sac tumor; Retroperitoneal neoplasms.
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Recebido em 4/8/97
Aceito pata publicação em 19/1/98
Trabalho realizado no Serviço de Cirurgia Geral do Hospital das Clínicas da Faculdade de Medicina da Universidade de São Paulo.
- 1. Oisen MM, Raffensperger FGC, Luck CR. Endodermal sinus tumor: a clinical and pathological correlation. J Ped Surg 1982; 17: 832- 840.
- 2. Hung WK, Bhutani R, Gersof SG, et al. Chemotherapy for primary retroperitoneal yolk sac tumor. Cancer 1981; 47: 19-21.
- 3. Harrns D, Janig U. Germ cell tumours of childhood - Report of 170 cases including 59 pure and partial yolk-sac tumours. Virchous Arch 1986; 409: 223-239.
- 4. Jones MA, Clement PB, Young RH. Primary yolk sac tumors of the mesentery - A report of two cases. Am Cl Pathl 1994; 101; 42-45.
- 5 . Bergljung L, Fager Lung M, Hammer E. Extragonadal endoderrnal sinus tumor - Report of a case. Acta Chir Scand 1975; 141: 688- 691.
Endereço para correspondência:
Datas de Publicação
-
Publicação nesta coleção
28 Jul 2010 -
Data do Fascículo
Jun 1998
Histórico
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Aceito
19 Jan 1998 -
Recebido
04 Ago 1997