We report a case of scleromyxedema with skin lesions in association with myopathy, esophageal dysfunction and paraproteinemia. During the disease course, the patient developed symptoms of cardiac failure related to a cardiomyopathy, a condition that has been described in up to 10% of patients with scleromyxedema. The clinical, etiologic and therapeutic aspects are discussed in this paper.
heart failure; myositis; mucinoses; paraproteinemias
