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Frontal fibrosing alopecia in association with Sjögren's syndrome: more than a simple coincidence* * Work performed at Hospital do Servidor Público Estadual do Estado de São Paulo (HSPE) - São Paulo (SP), Brazil.

Abstract

Frontal fibrosing alopecia is a distinctive form of scarring alopecia considered to be a clinical variant of lichen planopilaris. It predominantly occurs in postmenopausal women and has a slowly progressive course. It was first described by Kossard in 1994. Since then the number of reported cases has increased significantly. Coexistence of frontal fibrosing alopecia and autoimmune disorders - such as discoid erythematosus lupus and Sjögren's syndrome - may suggest a common pathogenic background among the diseases.

Keywords:
Alopecia; Autoimmunity; Discoid lupus erythematosus; Lichen planus; Sjögren's Syndrome

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