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Complete form of pachydermoperiostosis How to cite this article: Honório MLP, Bezerra GH, Costa VLC. Complete form of pachydermoperiostosis. An Bras Dermatol. 2020;95:98-101. ,☆☆ ☆☆ Study conducted at the Dermatology Service, Hospital Universitário Onofre Lopes, Natal, RN, Brazil.

Abstract

Pachydermoperiostosis (PDP) or primary hypertrophic osteoarthropathy (PHO) is a rare hereditary disease characterized by digital clubbing, pachydermia, and periostosis. Its pathogenesis is uncertain and the diagnosis is based on clinical and radiological data. A complete form of the syndrome is reported in a male patient with disease onset in adolescence, with compatible clinical and radiological findings, presenting the three cardinal findings as well as other associated manifestations, such as hyperhidrosis and acne.

KEYWORDS
Adolescent health; Heredity; Osteoarthropathy; Primary hypertrophic

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