Complex strabismus: a case report of hypoplasia of the third cranial nerve with an unusual clinical presentation

Estrabismo complexo: um caso relacionado à hipoplasia do terceiro nervo craniano com apresentação clínica incomum

ABSTRACT

Congenital cranial dysinnervation disorders are a group of complex strabismus syndromes that present as congenital and non-progressive ophthalmoplegia. The genetic defects are associated with aberrant axonal targeting onto the motoneurons, development of motoneurons, and axonal targeting onto the extraocular muscles. We describe here the surgical management of a 16-year-old boy who presented with complex strabismus secondary to hypoplasia of the third cranial nerve and aberrant innervation of the upper ipsilateral eyelid.

Keywords:
Oculomotor muscles/Innervation; Cranial nerve diseases; Oculomotor nerve; Strabismus; Ophthalmoplegia; Ca­se reports