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Síndrome de Russel ou síndrome de Diencefálica de emagreciemento

Russel's syndrome or diencephalic syndrome of emaciation: a case report

Resumos

Os autores relatam um caso de síndrome de Russel ou síndrome diencefálica do emagrecimento. Revisam a literatura disponível sobre o assunto e comentam a dificuldade do diagnóstico na fase inicial da doença.


The case of a four years old patient with Russel syndrome or diencephalic syndrome of emaciation is reported. The literature on the subject is reviewed. The difficulties for the diagnosis at the inicial fase of the illness are discussed.


Síndrome de Russel ou síndrome de Diencefálica de emagreciemento

Russel's syndrome or diencephalic syndrome of emaciation: a case report

Nelson Pires FerreiraI; Ércio Amaro de OliveiraII

IProfessor Assistente da UFRGS e Assistente do Instituto de Neurocirurgia de Porto Alegre

IIInstrutor de Ensino da UFRGS

RESUMO

Os autores relatam um caso de síndrome de Russel ou síndrome diencefálica do emagrecimento. Revisam a literatura disponível sobre o assunto e comentam a dificuldade do diagnóstico na fase inicial da doença.

SUMMARY

The case of a four years old patient with Russel syndrome or diencephalic syndrome of emaciation is reported. The literature on the subject is reviewed. The difficulties for the diagnosis at the inicial fase of the illness are discussed.

Instituto de Neurocirurgia — Hospital São Francisco, Pavilhão São José — Porto Alegre, RGS — Brasil

Trabalho realizado no Instituto de Neurocirurgia de Porto Alegre, apresentado no VIII Congresso da Sociedade Brasileira de Neurocirurgia (Brasília, 13-16 julho de 1970).

  • 1. AAS, K. Diencephalic syndrome of emaciation. Acta. Paediat. 52:161, 1963.
  • 2. CALDERA, R. & ROSSIER, A. Cachexie du jeune enfant par tumeur de l'hypothalamus. Ann. Pédiat. 38:613, 1962.
  • 3. CHOUX, M.; BAURAND, C; PIERRON, H. & VIGOUROUX, R. P. Lipo-atrophie cachectisante par tumeur de la partie antérieure du plancher du III ventricule (Syndrome de Russel). Neuro-chirurgie 15:59, 1969.
  • 4. CUSSEN, L. J. Diencephalic syndrome of early infancy. Med. Aust. 1:881, 1964.
  • 5. DÉCHENE, E.; JACOB, D.; CARRIER, C. & JEAN, C. Un syndrome diencéphalique associé a une tumeur cérébrale chez un nourrisson. Canad. Med. Ass. J. 93:319, 1965.
  • 6. DODS, L. A diencephalic syndrome of early infancy. Med. Aust. 1:222, 1967.
  • 7. HERMIER, M.; BRUNAT, M.; LAMIT, J.; HARTEMANN, E.; COTTON, J. B. & JEUNE, M. Les tumeurs cérébrales cachectisantes du nourrisson et du jeune enfant. Pediatrie 21:473, 1966.
  • 8. MANCIAUX, M.; MONTAUT, J.; THIRIET, M. & CHARLES, J. M. A propos d'un cas de cachexie diencephalique du nourrisson. Medicine Infant. 10:671, 1964.
  • 9. MARIE, J.; LEPINTRE, Mme.; FAURE, C.I.; LÉVEQUE, B. & PERELMAN, R. Cachexie progressive du nourrisson liée a une tumeur diencephalique. Arch, franc Pediat. 18:319, 1961.
  • 10. PETRORIUS, P. J. & HATTINGH, C. M. Diencephalic syndrome of emaciation associated with hypothalamic neoplasms. South Afr. Med. J. 40:419, 1966.
  • 11. PINSARD, N.; MARIANI, R.; SPRIET, A.; ROUX, J.; CHOUX, M. & BERNARD, R. Tumeur cachectisante du diencephalon chez un nourrisson. Marseille Méd. 105:35, 1968.
  • 12. SERINGE, Ph.; PLAINFOSSE, B.; HALLEZ, J. & BIRMAN, M. Un second cas de cachexie de l'enfant par tumeur de l'hypothalamus antérieur. Arch, franc Pédiat. 21:1221, 1964.
  • 13. RUSSEL, A. A diencephalic syndrome of emaciation in infancy and childhood. Arch. Dis. Child. 26:274, 1951.
  • 14. SMITH, K. R.; WEINBURG, W. A. & McALISTRE, H. W. Failure to thrive: the diencephalic syndrome of infancy and childhood. J. Neurosurg. 23:348, 1965.
  • 15. WHITE, P. T. & ROSS, A. T. Inanition syndrome in infants with anterior hipothalamic neoplasms. Neurology 13:974, 1963.

Datas de Publicação

  • Publicação nesta coleção
    19 Abr 2013
  • Data do Fascículo
    Jun 1971
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