The authors referred about one case of Bernard-Soulier Syndrome attended in the Otolaryngological Clinic of the Clinical Hospital of the Faculty of medicine of the Federal University of Goiás with nose, throat and gastro-intestinal manifestations. We discussing the most important considerations about clinical characteristics, diagnostic, treatment and evolution of the disease. We alert about the importance of think about bleeding disorder when the treatment is difficult in the recurrent epistaxis.
epistaxis; Bernard-Soulier