Bizzarri et al., 2015151. Jensen NS, Camargo TF, Bergamaschi DP. Índice de massa corpórea e perímetro da cintura são bons indicadores para classificação do estado nutricional de crianças. Ciênc Saúde Colet. 2016;21:1175-80. https://doi.org/10.1590/1413-81232015214.138712015 https://doi.org/10.1590/1413-81232015214...
1 |
2 |
Italy |
CF and CFRD group: 17. Control group CF, normal GTT: 52 |
Bruzzese et al., 20181212. Bruzzese E, Raia V, Ruberto E, Scotto R, Giannattasio A, Bruzzese D, et al. Lack of efficacy of Lactobacillus GG in reducing pulmonary exacerbations and hospital admissions in children with cystic fibrosis: a randomised placebo controlled trial. J Cyst Fibros. 2018;17:375-82. https://doi.org/10.1016/j.jcf.2017.10.014 https://doi.org/10.1016/j.jcf.2017.10.01...
|
3 |
Italy |
Lactobacillus rhamnosus GG group: 41 Placebo group: 40 |
Calella et al., 20181313. Calella P, Valerio G, Thomas M, McCabe H, Taylor J, Brodlie M, et al. Association between body composition and pulmonary function in children and young people with cystic fibrosis. Nutrition. 2018;48:73-6. https://doi.org/10.1016/j.nut.2017.10.026 https://doi.org/10.1016/j.nut.2017.10.02...
|
1 |
The United Kingdom |
69 |
Dentini et al., 20171414. Dentini P, Marson FA, Bonadia LC, Bertuzzo CS, Ribeiro AF, Levy CE, et al. Burkholderia cepacia complex in cystic fibrosis in a Brazilian reference center. Med Microbiol Immunol. 2017;206:447-61. https://doi.org/10.1007/s00430-017-0521-2 https://doi.org/10.1007/s00430-017-0521-...
|
1 |
Brazil |
Group A (BCC): 50. Group B (non-BCC): 134 |
Doulgeraki et al., 20171515. Doulgeraki A, Petrocheilou A, Petrocheilou G, Chrousos G, Doudounakis SE, Kaditis AG. Body composition and lung function in children with cystic fibrosis and meconium ileus. Eur J Pediatr. 2017;176:737-43. https://doi.org/10.1007/s00431-017-2906-z https://doi.org/10.1007/s00431-017-2906-...
|
1 |
Greece |
HMI: 19. Without HMI: 82 |
El Attar et al., 20171616. El Attar MM, Azab NM, Hamed DH, Tawfik AS. Growth assessment in Egyptian children with cystic fibrosis: a single center study. Egyptian Paediatric Association Gazette. 2017;65:21-4. https://doi.org/10.1016/j.epag.2017.01.001 https://doi.org/10.1016/j.epag.2017.01.0...
|
1 |
Egypt |
50 |
Engelen and Deutz, 20141717. Engelen MP, Com G, Deutz NE. Increased whole body hydroxyproline production as assessed by a new stable isotope technique is associated with hip and spine bone mineral loss in cystic fibrosis. Clin Nutr. 2014;33:1117-21. https://doi.org/10.1016/j.clnu.2013.12.008 https://doi.org/10.1016/j.clnu.2013.12.0...
|
1 |
The United States |
CF group: 15. Control group: 17 |
González-Jiménez et al., 20171818. González-Jiménez D, Muñoz-Codoceo R, Garriga-García M, Molina-Arias M, Álvarez-Beltrán M, García-Romero R, et al. Excess weight in patients with cystic fibrosis: is it always beneficial? Nutr Hosp. 2017;34:578-83. https://doi.org/10.20960/nh.620 https://doi.org/10.20960/nh.620...
|
1 |
Spain |
Pancreatic sufficiency: 371. Exocrine pancreatic insufficiency: 80 |
Goss et al., 20151919. Goss CH, MacNeill SJ, Quinton HB, Marshall BC, Elbert A, Knapp EA, et al. Children and young adults with CF in the USA have better lung function compared with the UK. Thorax. 2015;70:229-36. https://doi.org/10.1136/thoraxjnl-2014-205718 https://doi.org/10.1136/thoraxjnl-2014-2...
|
1 |
The United States and United Kingdom |
13,777; 3,968 |
Goss et al., 20182020. Goss CH, Sykes J, Stanojevic S, Marshall B, Petren K, Ostrenga J, et al. Comparison of nutrition and lung function outcomes in patients with cystic fibrosis living in Canada and the United States. Am J Respir Crit Care Med. 2018;197:768-75. https://doi.org/10.1164/rccm.201707-1541OC https://doi.org/10.1164/rccm.201707-1541...
|
2 |
Canada and the United States |
5,149; 37,772 |
Groleau et al., 20142121. Groleau V, Schall JI, Dougherty KA, Latham NE, Maqbool A, Mascarenhas MR, et al. Effect of a dietary intervention on growth and energy expenditure in children with cystic fibrosis. J Cyst Fibros. 2014;13:572-8. https://doi.org/10.1016/j.jcf.2014.01.009 https://doi.org/10.1016/j.jcf.2014.01.00...
|
3 |
The United States |
LXS group: 27. Placebo group: 36 |
Haack and Garbi-Novaes, 20142222. Haack A, Garbi-Novaes MR. Cystic fibrosis patients assisted by a program nutrition therapy: assessment of the use of supplements in patients colonized and non colonized by P. aeruginosa. Rev Invest Clin. 2014;66:136-43. PMID: 24960323
|
1 |
Brazil |
Without deficit: 34. With deficit: 13 |
Hauschild et al., 20162323. Hauschild DB, Barbosa E, Moreira EA, Ludwig Neto N, Platt VB, Piacentini Filho E, et al. Nutrition status parameters and hydration status by bioelectrical impedance vector analysis were associated with lung function impairment in children and adolescents with cystic fibrosis. Nutr Clin Pract. 2016;31:378-86. https://doi.org/10.1177/0884533615627157 https://doi.org/10.1177/0884533615627157...
|
1 |
Brazil |
CF group: 46. Group without CF: 24 |
Hauschild et al., 20182424. Hauschild DB, Rosa AF, Ventura JC, Barbosa E, Moreira EA, Ludwig Neto N, et al. Association of nutritional status with lung function and morbidity in children and adolescents with cystic fibrosis: a 36-month cohort study. Rev Paul Pediatr. 2018;36:31-8. https://doi.org/10.1590/1984-0462/;2018;36;1;00006 https://doi.org/10.1590/1984-0462/;2018;...
|
2 |
Brazil |
38 |
Hortencio et al., 20152525. Hortencio TD, Nogueira RJ, Marson FA, Hessel G, Ribeiro JD, Ribeiro AF. Factors impacting the growth and nutritional status of cystic fibrosis patients younger than 10 years of age who did not undergo neonatal screening. Rev Paul Pediatr. 2015;33:3-11. https://doi.org/10.1016/j.rpped.2014.11.004 https://doi.org/10.1016/j.rpped.2014.11....
|
2 |
Brazil |
52 |
Isa et al., 20162626. Isa HM, Al-Ali LF, Mohamed AM. Growth assessment and risk factors of malnutrition in children with cystic fibrosis. Saudi Med J. 2016;37:293-8. https://doi.org/10.15537/smj.2016.3.13476 https://doi.org/10.15537/smj.2016.3.1347...
|
1 |
Bahrain |
47 |
Kelly et al., 20162727. Kelly A, Schall J, Stallings VA, Zemel BS. Trabecular and cortical bone deficits are present in children and adolescents with cystic fibrosis. Bone. 2016;90:7-14. https://doi.org/10.1016/j.bone.2016.04.030 https://doi.org/10.1016/j.bone.2016.04.0...
|
1 |
The United States |
CF group: 97. Control group: 199 |
Ledder et al., 20152828. Ledder O, Oliver MR, Heine RG, Graham J, Volders E, Robinson PJ. Clinical audit results in earlier nutritional intervention in malnourished children with cystic fibrosis with improved outcome. J Paediatr Child Health. 2015;51:988-93. https://doi.org/10.1111/jpc.12888 https://doi.org/10.1111/jpc.12888...
|
2 |
Australia |
59 |
Okuro et al., 20172929. Okuro RT, Ribeiro MA, Ribeiro JD, Minsky RC, Schivinski CI. Alternative indexes to estimate the functional capacity from the 6-minute walk test in children and adolescents with cystic fibrosis. Respir Care. 2017;62:324-32. https://doi.org/10.4187/respcare.04625 https://doi.org/10.4187/respcare.04625...
|
1 |
Brazil |
CF group: 55. Control group: 185 |
Ong et al., 20173030. Ong T, Schechter M, Yang J, Peng L, Emerson J, Gibson RL, et al. Socioeconomic status, smoke exposure, and health outcomes in young children with cystic fibrosis. Pediatrics. 2017;139:e20162730. https://doi.org/10.1542/peds.2016-2730 https://doi.org/10.1542/peds.2016-2730...
|
2 |
The United States |
1,375 |
Papalexopoulou et al.,2018 3131. Papalexopoulou N, Dassios TG, Lunt A, Bartlett F, Perrin F, Bossley CJ, et al. Nutritional status and pulmonary outcome in children and young people with cystic fibrosis. Respir Med. 2018;142:60-5. https://doi.org/10.1016/j.rmed.2018.07.016 https://doi.org/10.1016/j.rmed.2018.07.0...
|
1 |
The United Kingdom |
CF group in study 1: 18. Study 2: 29 |
Sands et al., 20153232. Sands D, Umławska W, Zielińska A. A cross-sectional study of growth, nutritional status and body proportions in children and adolescents at a medical center specializing in the treatment of cystic fibrosis in Poland. Arch Med Sci. 2015;11:155-63. https://doi.org/10.5114/aoms.2015.49207 https://doi.org/10.5114/aoms.2015.49207...
|
1 |
Poland |
89 |
Sheikh et al., 20143333. Sheikh S, Zemel BS, Stallings VA, Rubenstein RC, Kelly A. Body composition and pulmonary function in cystic fibrosis. Front Pediatr. 2014;15;2:33. https://doi.org/10.3389/fped.2014.00033 https://doi.org/10.3389/fped.2014.00033...
|
1 |
The United States |
CF group: 208. Control group: 390 |
Welsh et al., 20143434. Welsh L, Robertson CF, Ranganathan SC. Increased rate of lung function decline in Australian adolescents with cystic fibrosis. Pediatr Pulmonol. 2014;49:873-7. https://doi.org/10.1002/ppul.22946 https://doi.org/10.1002/ppul.22946...
|
2 |
Australia |
98 |
Woestenenk et al., 20173535. Woestenenk JW, Gulmans VA, van der Ent CK, Houwen RH. Height assessment in the Dutch-origin pediatric cystic fibrosis population. Nutr Clin Pract. 2017;32:130-2. https://doi.org/10.1177/0884533616639109 https://doi.org/10.1177/0884533616639109...
|
1 |
Holland |
474 |